LinkedIn

 آمار

تعداد نشریات20
تعداد شماره‌ها1,149
تعداد مقالات10,518
تعداد مشاهده مقاله45,416,108
تعداد دریافت فایل اصل مقاله11,291,824
Nikmanesh, Yousef, Shokripour, Mansoureh, Mokhtari, Maral, Khazayi, Mahdi, Monabati, Ahmad, Rezayi, Ramin, Bahtouee, Mehrzad. (1402). Sporadic Lymphangioleiomyomatosis Disease: A Case Report. سامانه مدیریت نشریات علمی, 48(5), 516-521. doi: 10.30476/ijms.2022.95521.2689
Yousef Nikmanesh; Mansoureh Shokripour; Maral Mokhtari; Mahdi Khazayi; Ahmad Monabati; Ramin Rezayi; Mehrzad Bahtouee. "Sporadic Lymphangioleiomyomatosis Disease: A Case Report". سامانه مدیریت نشریات علمی, 48, 5, 1402, 516-521. doi: 10.30476/ijms.2022.95521.2689
Nikmanesh, Yousef, Shokripour, Mansoureh, Mokhtari, Maral, Khazayi, Mahdi, Monabati, Ahmad, Rezayi, Ramin, Bahtouee, Mehrzad. (1402). 'Sporadic Lymphangioleiomyomatosis Disease: A Case Report', سامانه مدیریت نشریات علمی, 48(5), pp. 516-521. doi: 10.30476/ijms.2022.95521.2689
Nikmanesh, Yousef, Shokripour, Mansoureh, Mokhtari, Maral, Khazayi, Mahdi, Monabati, Ahmad, Rezayi, Ramin, Bahtouee, Mehrzad. Sporadic Lymphangioleiomyomatosis Disease: A Case Report. سامانه مدیریت نشریات علمی, 1402; 48(5): 516-521. doi: 10.30476/ijms.2022.95521.2689

Sporadic Lymphangioleiomyomatosis Disease: A Case Report

Iranian Journal of Medical Sciences
مقاله 10، دوره 48، شماره 5، آذر 2023، صفحه 516-521    اصل مقاله (2.74 M)
نوع مقاله: Case Report(s)
شناسه دیجیتال (DOI): 10.30476/ijms.2022.95521.2689
نویسندگان
Yousef Nikmanesh1؛ Mansoureh Shokripour2؛ Maral Mokhtari2؛ Mahdi Khazayi3؛ Ahmad Monabati2؛ Ramin Rezayi3؛ Mehrzad Bahtouee* 3
1Gastroenterohepatology Research Center, Shiraz University of Medical Sciences, Shiraz, Iran
2Department of Pathology, School of Medicine, Shiraz University of Medical Sciences, Shiraz, Iran
3Department of Internal Medicine, School of Medicine, Bushehr University of Medical Sciences, Bushehr, Iran
چکیده
Pulmonary Lymphangioleiomyomatosis (LAM) is a rare disease of the lung and lymphatic system that primarily affects women of childbearing age. LAM is a progressive disease with a terrible prognosis, which worsens over time and is extremely difficult to treat. In this study, we discuss the case of a 31-year-old woman with LAM who was initially misdiagnosed with leiomyoma and the way that led to a true diagnosis and effective treatment. Following a precise diagnosis based on comprehensive clinical data and particular immunohistochemical tests, sirolimus treatment was initiated, and the patient entirely responded to the treatment. This case report demonstrated that LAM is an uncommon condition that is challenging to diagnose, which causes its treatment to be delayed.

تازه های تحقیق

Yousef Nikmanesh (Google Scholar)

Mehrzad Bahtouee (Google Scholar)

کلیدواژه‌ها
Lymphangioleiomyomatosis؛ Lung؛ Rare diseases؛ Pneumothorax
سایر فایل های مرتبط با مقاله
مراجع
  1. McCormack FX, Inoue Y, Moss J, Singer LG, Strange C, Nakata K, et al. Efficacy and safety of sirolimus in lymphangioleiomyomatosis. N Engl J Med. 2011;364:1595-606. doi: 10.1056/NEJMoa1100391. PubMed PMID: 21410393; PubMed Central PMCID: PMCPMC3118601.
  2. Gopalakrishnan V, Yao J, Steagall WK, Avila NA, Taveira-DaSilva AM, Stylianou M, et al. Use of CT Imaging to Quantify Progression and Response to Treatment in Lymphangioleiomyomatosis. Chest. 2019;155:962-71. doi: 10.1016/j.chest.2019.01.004. PubMed PMID: 30660784; PubMed Central PMCID: PMCPMC6533448.
  3. Johnson SR, Taveira-DaSilva AM, Moss J. Lymphangioleiomyomatosis. Clin Chest Med. 2016;37:389-403. doi: 10.1016/j.ccm.2016.04.002. PubMed PMID: 27514586.
  4. Kania BE, Jain S, West B, Courtney SW. Lymphangioleiomyomatosis: A Case Report and Review of Clinical Features and Management. Cureus. 2020;12:e8386. doi: 10.7759/cureus.8386. PubMed PMID: 32637268; PubMed Central PMCID: PMCPMC7331909.
  5. McCarthy C, Gupta N, Johnson SR, Yu JJ, McCormack FX. Lymphangioleiomyomatosis: pathogenesis, clinical features, diagnosis, and management. Lancet Respir Med. 2021;9:1313-27. doi: 10.1016/S2213-2600(21)00228-9. PubMed PMID: 34461049.
  6. Meraj R, Wikenheiser-Brokamp KA, Young LR, McCormack FX. Lymphangioleiomyomatosis: new concepts in pathogenesis, diagnosis, and treatment. Semin Respir Crit Care Med. 2012;33:486-97. doi: 10.1055/s-0032-1325159. PubMed PMID: 23001803.
  7. Taveira-DaSilva AM, Steagall WK, Moss J. Lymphangioleiomyomatosis. Cancer Control. 2006;13:276-85. doi: 10.1177/107327480601300405. PubMed PMID: 17075565.
  8. Goncharova EA, Goncharov DA, Lim PN, Noonan D, Krymskaya VP. Modulation of cell migration and invasiveness by tumor suppressor TSC2 in lymphangioleiomyomatosis. Am J Respir Cell Mol Biol. 2006;34:473-80. doi: 10.1165/rcmb.2005-0374OC. PubMed PMID: 16388022; PubMed Central PMCID: PMCPMC2644208.
  9. Almoosa KF, Ryu JH, Mendez J, Huggins JT, Young LR, Sullivan EJ, et al. Management of pneumothorax in lymphangioleiomyomatosis: effects on recurrence and lung transplantation complications. Chest. 2006;129:1274-81. doi: 10.1378/chest.129.5.1274. PubMed PMID: 16685019.
  10. Chu SC, Horiba K, Usuki J, Avila NA, Chen CC, Travis WD, et al. Comprehensive evaluation of 35 patients with lymphangioleiomyomatosis. Chest. 1999;115:1041-52. doi: 10.1378/chest.115.4.1041. PubMed PMID: 10208206.
  11. Rhee JA, Adial A, Gumpeni R, Iftikhar A. Lymphangioleiomyomatosis: A Case Report and Review of Literature. Cureus. 2019;11:e3938. doi: 10.7759/cureus.3938. PubMed PMID: 30937236; PubMed Central PMCID: PMCPMC6433088.
  12. Mitani K, Kumasaka T, Takemura H, Hayashi T, Gunji Y, Kunogi M, et al. Cytologic, immunocytochemical and ultrastructural characterization of lymphangioleiomyomatosis cell clusters in chylous effusions of patients with lymphangioleiomyomatosis. Acta Cytol. 2009;53:402-9. doi: 10.1159/000325340. PubMed PMID: 19697724.
  13. Pitts S, Oberstein EM, Glassberg MK. Benign metastasizing leiomyoma and lymphangioleiomyomatosis: sex-specific diseases? Clin Chest Med. 2004;25:343-60. doi: 10.1016/j.ccm.2004.01.014. PubMed PMID: 15099894.
آمار
تعداد مشاهده مقاله: 801
تعداد دریافت فایل اصل مقاله: 607


سامانه مدیریت نشریات علمی. قدرت گرفته از سیناوب