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Yousef Nikmanesh, Yousef x, Shokripour, Mansoureh, Mokhtari, Maral, Khazayi, Mahdi, Monabati, Ahmad, Rezayi, Ramin, Bahtouee, Mehrzad. (1401). Sporadic Lymphangioleiomyomatosis Disease: A Case Report. سامانه مدیریت نشریات علمی, (), -. doi: 10.30476/ijms.2022.95521.2689
Yousef x Yousef Nikmanesh; Mansoureh Shokripour; Maral Mokhtari; Mahdi Khazayi; Ahmad Monabati; Ramin Rezayi; Mehrzad Bahtouee. "Sporadic Lymphangioleiomyomatosis Disease: A Case Report". سامانه مدیریت نشریات علمی, , , 1401, -. doi: 10.30476/ijms.2022.95521.2689
Yousef Nikmanesh, Yousef x, Shokripour, Mansoureh, Mokhtari, Maral, Khazayi, Mahdi, Monabati, Ahmad, Rezayi, Ramin, Bahtouee, Mehrzad. (1401). 'Sporadic Lymphangioleiomyomatosis Disease: A Case Report', سامانه مدیریت نشریات علمی, (), pp. -. doi: 10.30476/ijms.2022.95521.2689
Yousef Nikmanesh, Yousef x, Shokripour, Mansoureh, Mokhtari, Maral, Khazayi, Mahdi, Monabati, Ahmad, Rezayi, Ramin, Bahtouee, Mehrzad. Sporadic Lymphangioleiomyomatosis Disease: A Case Report. سامانه مدیریت نشریات علمی, 1401; (): -. doi: 10.30476/ijms.2022.95521.2689

Sporadic Lymphangioleiomyomatosis Disease: A Case Report

Iranian Journal of Medical Sciences
مقالات آماده انتشار، اصلاح شده برای چاپ، انتشار آنلاین از تاریخ 20 اسفند 1401  XML اصل مقاله (2.75 M)
نوع مقاله: Case Report(s)
شناسه دیجیتال (DOI): 10.30476/ijms.2022.95521.2689
نویسندگان
Yousef x Yousef Nikmaneshorcid 1؛ Mansoureh Shokripour2؛ Maral Mokhtari2؛ Mahdi Khazayi3؛ Ahmad Monabati2؛ Ramin Rezayi3؛ Mehrzad Bahtouee email orcid 3
1Gastroenterohepatology Research Center, Shiraz University of Medical Sciences, Shiraz, Iran
2Department of Pathology, School of Medicine, Shiraz University of Medical Sciences, Shiraz, Iran
3Department of Internal Medicine, School of Medicine, Bushehr University of Medical Sciences, Bushehr, Iran
چکیده
Pulmonary Lymphangioleiomyomatosis (LAM) is a rare disease of the lung and lymphatic system that primarily affects women of childbearing age. LAM is a progressive disease with a terrible prognosis that worsens over time and is extremely difficult to treat. In this study, we discuss the case of a 31-year-old woman with LAM who was initially misdiagnosed with leiomyoma and the way which led to a true diagnosis and effective treatment. Following a precise diagnosis based on comprehensive clinical data and particular immunohistochemical tests, sirolimus treatment was initiated, and the patient entirely responded to the treatment. This case report demonstrated that LAM is an uncommon condition that is challenging to diagnose, which causes its treatment to be delayed.
کلیدواژه‌ها
Lymphangioleiomyomatosis؛ Lung؛ Rare diseases؛ Pneumothorax
مراجع
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