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Primitive Neuroectodermal Tumor of the Kidney in a 22-Year-Old Male: A Rare Entity | ||
Middle East Journal of Cancer | ||
مقاله 8، دوره 5، شماره 4، دی 2014، صفحه 233-236 اصل مقاله (3.57 M) | ||
نوع مقاله: Case Report(s) | ||
نویسندگان | ||
Veena Gupta؛ Rajeev Sen؛ Ashima Batra* ؛ Promil Jain | ||
Department of Pathology, Pt. B D Sharma PGIMS Rohtak, Haryana, India | ||
چکیده | ||
Primitive neuroectodermal tumors of the kidney are rare tumors representing about 1% of all sarcomas. Extraskeletal primitive neuroectodermal tumors may be found in the genitourinary tract, the testes, ovaries, uterus, or pancreas. Renal primitive neuroec- todermal tumors are frequently aggressive and almost 30% of all newly diagnosed cases present with distant metastases. Surgical intervention, intensive chemotherapeutic drugs and radiation therapy are the best choices for management. We discuss the case of a 22-year-old male who presented with a left renal mass. He underwent nephrectomy followed by histopathological examination. Microscopic and immunohistochemical examination revealed a primitive neuroectodermal tumor. | ||
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